FXN purified MaxPab rabbit polyclonal antibody (D01P)
产品名称： FXN purified MaxPab rabbit polyclonal antibody (D01P)
英文名称： FXN purified MaxPab rabbit polyclonal antibody (D01P)
产品编号： H00002395-D01P
产品价格： null
产品产地： 台湾
品牌商标： Abnova
更新时间： null
使用范围：
亚诺法生技股份有限公司（Abnova)
- 联系人 :
- 地址 : 台湾台北市内湖区洲子街 108 号 9 楼
- 邮编 : 11493
- 所在区域 : 台湾
- 电话 : +886-920**1152 点击查看
- 传真 : 点击查看
- 邮箱 : sales@abnova.com.tw
- Specification
- Product Description:
- Rabbit polyclonal antibody raised against a full-length human FXN protein.
- Immunogen:
- FXN (AAH48097.1, 1 a.a. ~ 210 a.a) full-length human protein.
- Sequence:
- MWTLGRRAVAGLLASPSPAQAQTLTRVPRPAELAPLCGRRGLRTDIDATCTPRRASSNQRGLNQIWNVKKQSVYLMNLRKSGTLGHPGSLDETTYERLAEETLDSLAEFFEDLADKPYTFEDYDVSFGSGVLTVKLGGDLGTYVINKQTPNKQIWLSSPSSGPKRYDWTGKNWVYSHDGVSLHELLAAELTKALKTKLDLSSLAYSGKDA
- Host:
- Rabbit
- Reactivity:
- Human
- Storage Buffer:
- In 1x PBS, pH 7.2
- Storage Instruction:
- Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
- Quality Control Testing:
- Antibody reactive against mammalian transfected lysate.
- MSDS:
Download
- Applications
- Western Blot (Transfected lysate)
- Western Blot analysis of FXN expression in transfected 293T cell line (H00002395-T01) by FXN MaxPab polyclonal antibody.
Lane 1: FXN transfected lysate(23.10 KDa).
Lane 2: Non-transfected lysate. - Protocol Download
- Entrez GeneID:
- 2395
- GeneBank Accession#:
- NM_000144
- Protein Accession#:
- AAH48097.1
- Gene Name:
- FXN
- Gene Alias:
- CyaY,FA,FARR,FRDA,MGC57199,X25
- Gene Description:
- frataxin
- Gene Ontology:
- Hyperlink
- Gene Summary:
- This nuclear gene encodes a mitochondrial protein which belongs to FRATAXIN family. The protein functions in regulating mitochondrial iron transport and respiration. The expansion of intronic trinucleotide repeat GAA results in Friedreich ataxia. Alternative splicing results in multiple transcript variants. [provided by RefSeq
- Other Designations:
- OTTHUMP00000021428
- Related Disease
- Cardiomegaly
- Cardiomyopathies
- Cardiovascular Diseases
- Cerebellar Ataxia
- Chronic Disease
- Diabetes Mellitus, Type 2
- Disease Progression
- Edema
- Fragile X Syndrome
- Fragile X syndrome
- Friedreich Ataxia
- Friedreich's ataxia
- Genetic Predisposition to Disease
- Glucose Intolerance
- Interview, Psychological
- Muscular Atrophy, Spinal
- Myocardial Infarction
- Myotonic Dystrophy
- Myotonic dystrophy